A condition causing fixation of the ear bones in the middle ear typically involving the stapes.
Genetic predisposition involving mutation in five collagen genes. Has a viral trigger and autoimmune component.
Conductive hearing loss results as the natural pattern of osseous remodelling becomes dysfunctional. Bone resorption occurs normally, however bone building or hyperosteoblast activity occurs and the stapes becomes hyperossified eventually impairing movement of the stapes and resultantly impairing sound conduction.
Stapedotomy using a CO2 Lazer.
A hole is created in the stapes to secure a prosthetic
This allows sound to bypass the fused stapes and transmit sound through to the oval window.