Abdominal Muscle Deficiency Syndrome (prune-belly syndrome)

condition of newborn babies, in which the baby has no abdominal muscles, so the stomach looks like a shriveled prune

Etiology:

rare birth defect affecting about 1 in 40,000 births.

Manifestations:

common symptoms triad:

  1. absence of abdominal muscles
  2. undescended testes
  3. abnormalities of the upper urinary tract affecting  urethra, bladder, ureters and kidneys.

Treatment:

Surgical correction of the congenital abnormalities

vesicostomy – allowing urine to drain through a stoma in the abdomen

orchiopexy – surgical correction of undescended testes in male infants

many infants progress rapidly to renal failure.

 

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